Article details
Rare Case of Susac Syndrome
Adel Ekladious
American Journal of Medical and Clinical Sciences
2021
Vol. 6
Issue 4
Pages 58-149
Susac syndrome is a rare autoimmune disease affecting the precapillary arteries of the brain,
eye and ears causing encephalopathy, branch retinal artery occlusion and sensorineural
hearing loss. It is underdiagnosed as it rarely presents with the classic triad. Encephalopathy
and branch retinal artery occlusion are curable if the treatment is started early, however
the sensorineural hearing loss may be irreversible. The disease course may be monocyclic,
polycyclic or chronic.
In this review present a case of Susac which was not diagnosed until late in the disease
course. Even though the three criteria manifested clinically, the patient was successfully
treated. We will also provide a clinical review on the disease based on our research from
the literature